Familial hemophagocytic lymphohistiocytosis in two brothers

• Main Authors: Gan, Gin Gin, Eow, Geok Im, Teh, A., Ng, S.C., Sangkar, J.V.
• Format: Article
• Language: English
• Published: Malaysian Medical Association 2004
• Subjects: R Medicine
• Online Access: http://eprints.um.edu.my/24581/1/Familial_Hemophagocytic_Lymphohistiocytosis.pdf; http://eprints.um.edu.my/24581/; http://www.e-mjm.org/2004/v59n1/Familial_Hemophagocytic_Lymphohistiocytosis.pdf

Familial hemophagocytic lymphohistiocytosis is a disorder which presents with fever, pancytopenia, liver dysfunction and also an increase in non-malignant histiocytes with prominent hemophagocytosis in various organs. It is usually difficult to distinguish from other hemophagocytic syndrome in the a...