Cholecysto-appendicostomy as partial internal biliary drainage in Progressive Familial Intrahepatic Cholestasis Type 1: A case report and review of literature

• Main Authors: Yik, Y.I., Othman, M.Y., Ng, R.T., Lee, W.S.
• Format: Article
• Published: Elsevier 2016
• Subjects: R Medicine
• Online Access: http://eprints.um.edu.my/18776/; http://dx.doi.org/10.1016/j.epsc.2015.11.009

Intractable pruritus secondary to bile salts retention in Progressive Familial Intrahepatic Cholestasis (PFIC) can be relieved surgically by diverting bile drainage from ileum to reduce bile salts reabsorption into entero-hepatic circulation. We are reporting on the successful biliary diversion in a...